ACADM Monoclonal Antibody-MB10483

ACADM Monoclonal Antibody Sizes: 50µl, 100µl Catalogue Numbers: MB10483-50, MB10483-100 Product: 50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% Sodium azide and 0.05% BSA Swiss-Prot: P11310 Host: Rabbit Reactivity: Human, Mouse, Rat Applications: WB, ICC/IF All Applications: WB: 1/500-1/1000 IF: 1/50-1/200 Background: This gene encodes the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Defects in this gene cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. Purification and Purity: Affinity Purified Storage and Stability: Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-